Choledochal cysts rare congenital abnormality of the biliary tree dilation of a portion of the bile duct affects 1 in,000 to 1 in 2,000,000 present in girls 3 times more than boys causes 2%5% of extrahepatic neonatal jaundice 20% become symptomatic in adulthood. Choledochal cyst october 2010 background congenital anomalies of the bile ducts. Symptoms of choledochal cysts in infants include an enlarged liver and jaundice. Choledochal cysts are uncommon and of unknown cause, with an incidence of 0. Oncocytic cysts in parotid gland college of physicians.
Urachal cysts can develop at any age, but typically affect older children and adults. We use your linkedin profile and activity data to personalize ads and to show you more relevant ads. As the condition is not confined to the extrahepatic bile duct, the term choledochal cyst is in fact a misnomer and bile duct cyst or biliary cyst is probably more appropriate. Presentation and outcomes of choledochal cysts in children. There arefour basic types of choledochal cysts based on where they appear. First reported by vater and ezler 1 in 1723, choledochal cysts ccs are rare cystic dilations of the biliary tract. Laparoscopic excision of choledochal cysts has increasingly gained acceptance and applicability since its first description by farello 1, 2, 3. Their diagnosis is difficult, particulary in adults. To prevent costintensive and potentially lifethreating complications, a choledochal cyst must be considered in the differential diagnosis whenever the rather common diagnosis of a hepatic cyst is considered. Treatment varies depending on type of choledochal cyst, but type i and iv cysts typically undergo surgical excision and reconstruction by rouxeny hepaticojejunostomy left this graphic shows the todani classification of choledochal cysts. Left untreated, this frequently lead to recurrent cholangitis inflammation and infection in the bile ducts or pancreatitis inflammation of the pancreas. Choledochal cysts ccs are single or multiple dilatations of the intrahepatic or extrahepatic biliary tree. Most are harmless, but they should be removed when possible because they occasionally may change into malignant growths, become infected, or obstruct a gland.
We recommend that choledochal cyst be considered as a differential diagnosis in all patients with dilated bile ducts, especially when. It is a rare condition occurring more commonly in the developing countries 100 times more common in japan than in the west and these congenital lesions have a female bias 4 times more commonly than in males. Patient was symptom free on followup, and excision of the choledochal cyst was planned. Urachal cyst genetic and rare diseases information. We report a case of a female infant with an antenatally diagnosed choledochal cyst.
Future complications include cholangitis and a 2% risk of malignancy, which may develop in any part of the biliary tree. Evidencebased information on choledochal cyst from hundreds of trustworthy sources for health and social care. If left untreated, they can cause morbidity and mortality from recurrent cholangitis, pancreatitis, sepsis, liver abscesses and cholangiocarcinoma. This case report demonstrates the diagnostic and therapeutic pitfalls. Hello dr xxxxxxx xxxxx,my sister is diagnosed with choledocal cyst,what are the treatment options,which doctor should i go for.
Le, md, philippe jeanty, md, phd course objectives. For type iii can offen be managed with endoscopicsphincterotomy or endoscopic resectionfor type v as with type iva cysts, some patients with type v cysts will eventuallyrequire liver transplantation. Permission is granted to copy, distribute andor modify this document under the terms of the gnu free documentation license, version 1. A choledochal cyst is a cyst hollow outpouching of the bile ducts. Choledochal cyst is a topic covered in the pediatric surgery nat to view the entire topic, please sign in or purchase a subscription apsa pediatric surgery library combines pediatric surgery not a textbook nat with apsa expert, a powerful platform for earning moc cme credits all powered by unbound medicine. First found western literature 1723 vater and ezler. The lesions containing oncocytic cells in a salivary gland include oncocytomas,1 warthins tumour, oncocytic adenocarcinoma and mucoepidermoid carcinomas. Choledochal cyst is a relatively rare disease in the west, and thus most cases have originated from asia.
The vast majority of oral malignancies are squamous cell carcinoma. Until now, no unifying etiologic theory exists for choledochal cysts, but most literature would conclude they are congenital bile duct anomalies. Publications home of jama and the specialty journals of. Choledochal cysts can present dramatically in infancy. Choledochal cysts are congenital anomalies, which present as either isolated or combined dilatations of the extra and intrahepatic biliary tree. Unfortunately, no further imaging was made available for correlation with the ultrasound findings. Bile duct surgery with total cyst removal is the definitive treatment for choledochal cysts. Although it normally disappears prior to birth, part of the urachus may remain in some people. Endoscopic retrograde cholangio pancreatogram ercp confirmation and endoscopic minor papilla stenting and sphincterotomy were done. Choledochal cysts are diagnosed in children and adults, although most 80% develop in children younger than 10 years.
The parotid gland away from the cyst showed a reactive lymph node. In older people, the cysts cause abdominal pain, jaundice, cholangitis, gallstones, and pancreatitis. Choledochal cyst is a congenital cystic dilatation of the bile tract. Completeradical cyst excision plus rouxeny hepatojeju nostomy has substantially reduced the incidence of postop erative. Rattner et al 3 also suggested that choledochal cyst is the most obvious manifestation of a more widespread pancretobiliary duct dysplasia. Management of adult choledochal cysts a 15year experience. Complications after cyst excision with hepaticoenterostomy for choledochal cysts and their surgical management in. A copy of the license is included in the section entitled gnu free documentation license. Choledochal cyst is an uncommon congenital disease of the biliary tract in the uk. Choledochal cyst definition of choledochal cyst by. However, the diagnosis may be delayed until adulthood due to paucity of symptoms. Kasais procedure was performed after cyst excision in both case to permit free drainage of bile.
Thus our report of multilocular cyst in the pancreas and choledochal cyst in a child could support their theory that choledochal cyst is part of a widespread pancretobiliary duct dysplasia. In this series a correct preoperative diagnosis was established in eight of the ten patients. Choledochal cysts can form in the part of the bile duct inside of the liver intrahepatic or outside the liver extrahepatic. Choledochal cyst is usually a surgical problem of infancy and childhood. Discussion pancreas divisum results from a failure of the. Type 1 a cyst of the extrahepatic bile duct, accounting for up to 90% of all choledochal cysts.
There are several different types of choledochal cysts. Uptodate, electronic clinical resource tool for physicians and patients that provides information on adult primary care and internal medicine, allergy and immunology, cardiovascular medicine, emergency medicine, endocrinology and diabetes, family medicine, gastroenterology and hepatology, hematology, infectious diseases, nephrology and. There are five main types of choledochal cyst with several recognised subtypes. In this study, the clinical difference of laparoscopic surgery and laparotomy in the treatment of pediatric choledochal cyst was analyzed to explore the advantages, disadvantages of laparoscope in the treatment of congenital choledochal cyst, which provides a reference and theoretical basis for the application of laparoscope in the treatment of.
The clinical manifestations in older children and adults are more protean. Choledochal cyst childrens liver disease foundation. Ppt choledochal cysts powerpoint presentation free to. Choledochal cyst article about choledochal cyst by the. Click export csv or ris to download the entire page or use the checkboxes to select a subset of records to download. Choledochal cysts, or dilatation of the common bile duct, were fi rst reported by douglas in 1852. The study is compatible with dilatation of entire extrahepatic bile duct, thats also known as a true choledochal cyst.1387 711 1410 436 955 734 451 464 764 1002 438 300 850 842 1161 1576 1322 1203 204 459 1575 61 267 1005 964 455 14 30 56 71 385 741 464 503 322 900 244